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CompletedNCT03058848PKU StartUpdated Feb 16, 2024

Evaluation of PKU Start

An interventional study of PKU Start in Phenylketonuria and Inborn Errors of Metabolism, sponsored by Vitaflo International, Ltd. Completed at 3 sites in United Kingdom. Open to participants aged 4 Weeks to 2 Years. Per ClinicalTrials.gov, last updated 2024-02-16.

Sponsored by Vitaflo International, Ltd · Not applicable, Interventional, and Treatment

Phase
Not applicable
Study type
Interventional
Enrollment
10
Allocation
Not applicable
Ages
4 Weeks to 2 Years
Sex
All
01

Study summary

To evaluate the acceptability, tolerance and effect on metabolic control of PKU Start, a new Phe free protein substitute for the dietary management of PKU in infants from birth.

Read the detailed description

This is an assessment of ten (10) infants who require a protein restricted diet that is low in Phe. Infants who routinely use a Phe free infant formula as part of their dietary therapy will be recruited for a 28-day assessment of PKU Start, to evaluate tolerance and acceptability.

The outcome of this assessment will be used in a submission to the regulatory authorities, Advisory Committee on Borderline Substances (ACBS), for PKU Start to become reimbursable on prescription in the UK.

The participant's dietitian will advise on an appropriate amount of PKU Start based on individual requirements. Parents/carers will be asked to substitute their usual Phe-free infant formula with PKU Start for one (1) month. The sponsor will supply PKU Start free of charge.

Prior to starting PKU Start, parents/carers will be asked to record information about the infant's usual GI tolerance and feeding pattern for a period of three (3) days, to allow for comparison between their existing formula and PKU Start.

They will be asked to record information about the following:

Stools Vomiting and Spit-up Feed / Fluid Intake and Compliance Phenylalanine Levels Final Evaluation about the presentation of the product, ease of preparation and how PKU Start flowed through the teat of a bottle.

02

Conditions studied

  • Phenylketonuria
  • Inborn Errors of Metabolism

Keywords

  • Phenylketonuria
  • PKU
  • Metabolism
  • Metabolic
  • Control
  • Acceptability
03

Who can participate

Ages eligible
4 Weeks to 2 Years
Sexes eligible
All
Accepts healthy volunteers
No

Inclusion criteria

  1. A diagnosis of classical or severe PKU on new-born screening (For the purposes of this study, 'severe' is defined as phe concentrations between 120 and 600 µmol/L at diagnosis)
  2. Taking a minimum of one (1) feed of a Phe-free infant formula
  3. A minimum period of four (4) weeks from the time of diagnosis to initial approach to parents

Exclusion criteria

Exclusion Criteria:

  1. Diagnosed with mild PKU or hyperphenylalaninaemia (For the purposes of this study, 'mild' is defined as phe concentrations between 120 and 600 µmol/L at diagnosis)
  2. Diagnosis of a congenital condition
04

Study design

Phase
Not applicable
Primary purpose
Treatment
Allocation
Not applicable
Intervention model
Single group
Masking
None (open label)
Enrollment
10 participants (actual)

Study arms

  • Experimental
    Consumption of PKU Start

    Daily feed, substituting the participant's normal phe-free formula for PKU Start.

    Dietary Supplement: PKU Start

Interventions

  • Dietary supplementPKU Start

    PKU Start is a powdered, phenylalanine-free, infant formula, containing essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals, trace elements and long chain polyunsaturated fatty acids (LCPs); Arachidonic acid (AA) and Docosahexaenoic acid (DHA). It is suitable for use from birth. The recommended amount of the product for each participant will be determined and prescribed by a dietitian.

05

What researchers measure

Primary outcomes

  1. Product compliance daily diary

    Quantitative assessments from subject questionnaires that allow evaluation of compliance with the study product, i.e. actual versus prescribed intake.

    Time frame: Days 1-28

  2. GI tolerance daily diary

    Qualitative assessments from subject questionnaires that allow evaluation of the gastro-intestinal tolerance of the study product.

    Time frame: Days 1-28

  3. Ease of use questionnaire

    Qualitative assessment from subject questionnaire that allows evaluation of the ease of use of the study product.

    Time frame: Day 29

  4. Daily phenylalanine control

    Collection of quantitative data regarding phenylalanine control using routine biochemical testing

    Time frame: Days 1-28

06

Study locations

3 sites
  • NHS Greater Glasgow and Clyde
    Glasgow, Lanarkshire G51 4TF, United Kingdom
  • Birmingham Children's Hospital NHS Foundation Trust
    Birmingham, West Midlands B4 6NH, United Kingdom
  • Bradford Teaching Hospitals NHS Foundation Trust
    Bradford, West Yorkshire BD5 0NA, United Kingdom
07

References and documents

Individual participant data

Plan to share: Undecided

No publications or documents are linked to this record.

08

Registry details

Key details

Study ID
NCT03058848
Lead sponsor
Vitaflo International, Ltd
Responsible party
Sponsor
First posted
Feb 23, 2017
Start date
Mar 6, 2017
Primary completion
Sep 15, 2017
Completion
Sep 15, 2017
Last update
Feb 16, 2024

Study contacts

Anita MacDonald
principal investigator · Birmingham Women's and Children's NHS Foundation Trust

Oversight

Data monitoring committee
No
FDA-regulated drug
No
FDA-regulated device
No
View the source record on ClinicalTrials.gov ↗

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