ClinicalTrials.gg
RecruitingNCT07673809Updated Jun 29, 2026

A Study to Evaluate the Tolerability, Safety and Efficacy of GNR-097 Gene Therapy in Pediatric Patients With Duchenne Muscular Dystrophy

A Phase 1/2 interventional study of GNR-097 and Placebo followed by GNR-097 in Duchenne Muscular Dystrophy, sponsored by AO GENERIUM. Recruiting at 6 sites in 2 countries. Open to male participants aged 4 Years to 9 Years. Per ClinicalTrials.gov, last updated 2026-06-29.

Sponsored by AO GENERIUM · Phase 1/2, Interventional, and Treatment

From the registry’s dates

  • Registered 8 months after the study started (first participant enrolled Sep 2025, registered Jun 2026).
  • Started Sep 2025; still recruiting 1 year 1 month later.
Phase
Phase 1/2
Study type
Interventional
Enrollment
32
Allocation
Randomized
Ages
4 Years to 9 Years
Sex
Male
01

Study summary

The study will evaluate the tolerability, safety and efficacy of gene therapy product in boys with Duchenne muscular dystrophy (DMD). In Phase I the participants will be included in two sequential dose cohorts with increasing doses of the investigational product. Based on the results of Phase I, the dose of the investigational product for use in Phase II will be determined. Phase II is a randomized, single-blind, placebo-controlled study. The participants who are randomized to the placebo arm will have an opportunity for treatment with gene therapy at the beginning of the second year.

02

Conditions studied

  • Duchenne Muscular Dystrophy

Keywords

  • Duchenne Muscular Dystrophy
  • DMD
  • Ambulatory
  • Gene Therapy
  • Micro-dystrophin
  • AAV
  • AAV9
03

In context

Muscular Dystrophy, Duchenne

481 studies on the registry are indexed under Muscular Dystrophy, Duchenne; 108 are open to participants now.

This study's planned enrollment of 32 is above the median of 26 across 332 interventional studies indexed under Muscular Dystrophy, Duchenne.

Browse Muscular Dystrophy, Duchenne studies →

Lead sponsor

AO GENERIUM is the lead sponsor of 31 studies on the registry; 3 are open to participants now.

Counted across the registry records on this site, refreshed daily.

04

Who can participate

Ages eligible
4 Years to 9 Years
Sexes eligible
Male
Accepts healthy volunteers
No

Go through the criteria one by one — yes, no or not sure — and take the list to your doctor or the study team. Kept in this browser only.

Inclusion criteria

  1. Written for participation in the trial.
  2. Ambulatory boys aged 4-9 years with a documented diagnosis of DMD and clinical manifestations of the disease.
  3. A frameshift mutation or nonsense mutation in the DMD gene.
  4. Сreatine phosphokinase level >5000 U/L.
  5. Binding antibody titer to AAV9 ≤1:50 [method: ELISA].
  6. The patient is able to interact with the study physician and perform tests to assess functional activity.
  7. Results of functional activity assessment tests at screening (at least in one of the two attempts performed on different days):

    • NSAA ≥22;
    • time to rise from a supine position without using surrounding objects or furniture \<5 sec;
    • 6MWT distance ≥350 m.
  8. The patient received oral glucocorticosteroids at a stable dose for ≥12 weeks prior to signing the Informed Consent Form, and it is planned that glucocorticosteroids will be continued during the screening stage and after the patient's inclusion in the study.
  9. For patients receiving deflazacort at study entry: switching the patient from deflazacort to prednisolone, in the opinion of the investigator, will not result in a significant deterioration in the patient's health.
  10. The patient has been immunized with a vaccine against meningococcal serotypes A, C, Y, W135 (and B, if available) no later than 4 weeks prior to administration of GNR-097/placebo, and the immunization period expires no more than three months after the expected date of administration of GNR-097/placebo.

Exclusion criteria

Exclusion Criteria:

  1. to any component of GNR-097 or placebo.
  2. Patient with cognitive impairment or a sedentary lifestyle that, in the opinion of the investigator, may interfere with the development or manifestation of motor activity.
  3. Mutations in exons 8 and/or 9 of the DMD gene; for patients planned for inclusion in Cohort A, additionally: mutations in exons 1-17 and/or 59-71 of the DMD gene.
  4. Clinical signs of cardiomyopathy, including (Simpson) \<40% based on echocardiography performed during screening.
  5. to magnetic resonance imaging.
  6. History of any disease, with the exception of drug-compensated autoimmune thyroiditis.
  7. History of tuberculosis; positive or indeterminate result of Diaskintest® TigraTest® or T-SPOT.TB screening.
  8. Positive results of tests for , , or screening.
  9. Acute infectious diseases that resolved less than 4 weeks before administration of GNR-097/placebo.
  10. Immunization with a less than 3 months before administration of GNR-097/placebo OR immunization with any inactivated vaccine less than 4 weeks before administration of GNR-097/placebo.
  11. Abnormal laboratory parameters:

    • GGT level is more than three ;
    • total >50.0 μmol/L (except for patients with a confirmed diagnosis of Gilbert's syndrome);
    • creatinine >160.0 μmol/L;
    • \<80 or >180 g/L;
    • white blood cell count >18,500/μL;
    • count below the lower limit of normal.
  12. History of taking antisense oligonucleotides, ataluren, gene therapy using vector constructs, or cell therapy.
  13. Use of drugs other than glucocorticosteroids less than 12 weeks prior to signing the Form.
  14. Participation in clinical trials less than 6 months prior to signing the Informed Consent Form.
  15. Unwillingness or inability of the patient and/or their parent/legal guardian to comply with the protocol requirements and/or the trial procedures.
  16. Other diseases or conditions not listed above that, in the opinion of the physician investigator and/or the Sponsor, prevent the patient from participating in the trial, including for safety reasons.
Terms in these criteria, in plain language(14)

Underlined terms in the criteria open these too. Explained by clinicaltrials.gg, not part of the registry record. The study team decides who can take part.

Informed consent

Before you join, the study team explains what taking part involves — its purpose, what happens, the risks and possible benefits — and answers your questions, so you can decide freely. Consent is usually recorded on a form (the informed consent form, ICF) signed by you or, where the law allows, by someone legally authorised to decide for you.

You can keep asking questions during the study, you are told of new information that matters, and you can choose to leave at any time.

Hypersensitivity

An allergy, or another reaction of the immune system, to a substance. “Hypersensitivity to the study drug” means a known allergic reaction to it — not every side effect a medicine can have.

LVEF (left ventricular ejection fraction)

The share of blood the heart’s main pumping chamber (the left ventricle) pushes out with each beat, measured by an echocardiogram (heart ultrasound) or a MUGA scan. About 50–70% is normal.

Contraindication

A reason a treatment, test or procedure should not be given to a particular person, such as an allergy, another illness or a medicine they take.

Autoimmune disease

A condition in which the immune system attacks the body’s own tissues, such as rheumatoid arthritis, lupus, psoriasis, type 1 diabetes or inflammatory bowel disease.

Immunotherapy studies often leave out active autoimmune disease, and some name exceptions, such as thyroid disease on replacement hormone. Check the exceptions this study lists.

Hepatitis B tests

Hepatitis B is a virus that infects the liver. These are separate tests: HBsAg positive usually means a current infection (a recent vaccination can briefly cause it too); total anti-HBc (HBcAb) positive means an infection now or in the past; HBV DNA measures how much virus is in the blood.

Some studies accept a past infection if HBV DNA is undetectable, sometimes with antiviral medicine during the study. Check what this study allows.

Hepatitis C tests

Hepatitis C is a virus that infects the liver. An HCV antibody test can stay positive after an infection has cleared (and is occasionally positive without one); an HCV RNA test shows whether the virus is there now.

After treatment, hepatitis C counts as cured when HCV RNA is still undetectable 12 weeks or more after the treatment ended. Studies often accept people cured this way.

HIV

The human immunodeficiency virus, which weakens the immune system.

Many studies now accept people whose HIV is controlled on treatment, judged by the viral load and the CD4 count. Check the limits this study sets.

Live vaccines

Vaccines made with a weakened form of the germ, such as measles–mumps–rubella (MMR), chickenpox and yellow fever. They can be risky when the immune system is weakened. Flu injections are not live; the nasal flu spray is.

ULN (upper limit of normal)

The top of the normal range for a blood test, as set by the laboratory that runs it. Each lab prints its own range next to your result.

“≤ 2.5 × ULN” means the result can be up to two and a half times that top value.

Bilirubin

A yellow substance made when red blood cells are broken down, which the liver clears. A high level can mean a problem with the liver or the bile ducts.

Criteria often allow more for people with Gilbert’s syndrome, a harmless inherited condition that raises bilirubin.

Hemoglobin (Hb)

The protein in red blood cells that carries oxygen. A low level is anaemia, which can cause tiredness and breathlessness. Measured in g/dL or g/L (9 g/dL is 90 g/L).

Platelets

Blood cells that help blood clot. Too few raises the risk of bleeding and bruising. A usual adult range is about 150–400 × 10⁹/L (150,000–400,000 per µL); each lab has its own reference range.

Immunosuppression

A weakened immune system. It can come from an illness, such as HIV or some blood cancers, or from medicines that turn the immune system down, for example after an organ transplant or for an autoimmune disease; steroids at higher doses count.

Read whether the line is about a condition or about medicines, and which medicines and doses it means.

05

Study design

Phase
Phase 1 / Phase 2
Primary purpose
Treatment
Allocation
Randomized
Intervention model
Parallel assignment
Masking
Triple (Participant, Care provider, Outcomes assessor)
Enrollment
32 participants (estimated)

Study arms

  • Experimental
    GNR-097

    Participants will receive single intravenous (IV) infusion of GNR-097 on Day 1.

    Genetic: GNR-097

  • Placebo comparator
    Placebo followed by GNR-097

    In Phase II participants will receive matching placebo IV infusion on Day 1. Then, they will have the opportunity to receive a single IV infusion of GNR-097 at the beginning of the second year.

    Genetic: Placebo followed by GNR-097

Interventions

  • GeneticGNR-097

    Single IV infusion of GNR-097 (recombinant adeno-associated virus, serotype 9 (AAV9) carrying a truncated human dystrophin gene (micro-dystrophin)).

  • GeneticPlacebo followed by GNR-097

    Single IV infusion of matching placebo followed by single IV infusion of GNR-097 at the beginning of the second year.

06

What researchers measure

Primary outcomes

  1. Number and percentage of participants with treatment-emergent adverse events (AEs), AEs of special interest and serious adverse events (SAEs)

    AEs of special interest include immune-mediated myositis, myocarditis, thrombotic microangiopathy and hemolytic uremic syndrome

    Time frame: Baseline to End of Study (Week 104)

Other outcomes

  1. Antibodies to AAV9 and microdystrophin

    Presence and titer of binding and neutralizing antibodies to AAV9 and total antibodies to microdystrophin as measured by ELISA

    Time frame: Baseline to End of Study (Week 104)

  2. Quantity of dystrophin and microdystrophin in biopsied muscle

    Measured by Western blot

    Time frame: Baseline, Week 12

  3. Percentage of dystrophin-positive muscle fibers in biopsied muscle

    Measured by immunohistochemistry (IHC)

    Time frame: Baseline, Week 12

  4. Intensity of immunofluorescence of muscle fibers in biopsied muscle when they are stained for dystrophin

    Measured by IHC

    Time frame: Baseline, Week 12

  5. North Star Ambulatory Assessment (NSAA) score

    Confirmed by independent assessor

    Time frame: Baseline to End of Study (Week 104)

  6. Time to rise from the floor from a supine position

    Time to rise from the floor from a supine position

    Time frame: Baseline to End of Study (Week 104)

  7. Six minute walk test (6MWT) distance

    Confirmed by independent assessor

    Time frame: Baseline to End of Study (Week 104)

07

Study locations

6 of 6 sites recruiting
  • Republican Scientific and Practical Center Mother and Child
    Minsk, 220053, Belarus
    Recruiting
    • Irina V. Zhevneronok, Ph.D. · Principal investigator
  • Russian Children's Clinical Hospital
    Moscow, 117513, Russia
    Recruiting
    • Svetlana V. Mikhailova, Dr. Med. Sci. · Principal investigator
  • National Medical Research Center for Children
    Moscow, 119991, Russia
    Recruiting
    • Lyudmila M. Kuzenkova, Dr. Med. Sci., professor · Principal investigator
  • Veltischev Research and Clinical Institute for Pediatrics and Pediatric Surgery of the Pirogov Russian National Research Medical University
    Moscow, 125412, Russia
    Recruiting
    • Dmitry V. Vlodavets, Dr. Med. Sci. · Principal investigator
  • Saint Petersburg State Pediatric Medical University
    Saint Petersburg, 194100, Russia
    Recruiting
    • Vasily M. Suslov, Ph.D. · Principal investigator
  • Regional Children's Clinical Hospital
    Yekaterinburg, 620149, Russia
    Recruiting
    • Olga A. Lvova, Dr. Med. Sci. · Principal investigator
08

References and documents

Individual participant data

Plan to share: Undecided

No publications or documents are linked to this record.

09

Timeline

Tracking since Sep 25, 2026
ElapsedEstimatedEstimated, not yet reachedSimilar studies: half by the dot; the band is the middle halfHalf of similar studies reached it by the dot; the band is the middle half, from a quarter to three quarters

Started Sep 2025 (actual). Primary completion is estimated for Aug 2029, 46 months after the start.

Of 23 phase 1/2 interventional studies under Muscular Dystrophy, Duchenne, half reached primary completion within 50 months of starting (the median), counting those still running; a quarter within 24 and three quarters within 63. This study's planned 46 months is close to that.

How these figures are worked out, and which studies are left out of them.

Registered
Jun 23, 2026
First posted
Jun 29, 2026
StartActual
Sep 30, 2025
Primary completionEst.
Aug 2, 2029
CompletionEst.
Aug 2, 2029
Last update
Jun 29, 2026
What these dates mean
Start.
When the first participant enrolled; while estimated, when the study expects to open to recruitment.
Primary completion.
When the last participant was examined or treated to collect data for the study's main question, its primary outcome. A study that stopped early gives the date its data collection stopped.
Completion.
When the last participant's last visit took place, for every outcome, secondary ones and side effects included: the end of the study. Often later than primary completion, sometimes the same day.
Actual and Est.
Actual means the registry says the date has happened. Est. (estimated) is a date the sponsor plans or expects. It can still move, and the sponsor is expected to change it to actual once it has passed.
No changes since tracking began. The registry record was last updated on Jun 29, 2026, before this site started recording changes on Sep 25, 2026. Its history is on ClinicalTrials.gov ↗
10

Registry details

Key details

Study ID
NCT07673809
Lead sponsor
AO GENERIUM
Responsible party
Sponsor
First posted
Jun 29, 2026
Start date
Sep 30, 2025
Primary completion
Aug 2, 2029 (estimated)
Completion
Aug 2, 2029 (estimated)
Last update
Jun 29, 2026

Study contacts

Elena I. Zagoruyko, M.D.
Contact
eizagoruiko@generium.ru
+7 (926) 344 84 48
Oksana A. Markova, M.D.
Contact
oamarkova@generium.ru
+7 (985) 441 89 59
Oksana A. Markova, M.D.
study chair · AO GENERIUM

Oversight

Data monitoring committee
Yes
FDA-regulated drug
No
FDA-regulated device
No
View the source record on ClinicalTrials.gov ↗

Interested in this study?

Eligibility is decided by the study team. Share this record with your doctor or contact the team directly.

Contact study team

Follow this study

Get an email when the registry record changes — status, dates, results — or when someone posts here.

Sign in to follow

Discussion

Questions and observations about this study, from anyone following it. Not medical advice, and not a channel to the study team — their contact details are on the registry record.

Sign in to join the discussion. Reading takes no account; posting does. You choose a display name, and a pseudonym is the default.

Nothing here yet. If you are running this trial, taking part in it, or weighing whether to, this is the place to say so.

Start the discussion