CClinicalTrials.gg
CompletedNCT03257462Updated Oct 22, 2025Results posted

Study of SPR001 in Adults With Classic Congenital Adrenal Hyperplasia

A Phase 2 interventional study of SPR001 in Congenital Adrenal Hyperplasia and CAH - Congenital Adrenal Hyperplasia, sponsored by Spruce Biosciences. Completed at 9 sites in United States. Open to participants aged 18 Years and older. Per ClinicalTrials.gov, last updated 2025-10-22.

Sponsored by Spruce Biosciences · Phase 2, Interventional, and Treatment

Phase
Phase 2
Study type
Interventional
Enrollment
24
Allocation
Non-randomized
Ages
18 Years and older
Sex
All
01

Study summary

This is a multicenter Phase 2, multiple dose, dose escalation study to evaluate the safety, pharmacokinetics (PK), pharmacodynamics (PD), and efficacy of SPR001 in adult patients with classic congenital adrenal hyperplasia (CAH).

Read the detailed description

This is a 6-week, multiple-dose, dose escalation study of SPR001 for the treatment of adults with classic CAH. After screening, eligible patients will be enrolled into a 6-week treatment period followed by a 4-week washout/safety follow-up period.

It is initially planned that up to approximately 18 patients in 2 dose cohorts will be enrolled. Additional patients or dose groups may be considered based upon specific safety, PK/PD, and/or efficacy findings, or if an active dose has not yet been reached.

SPR001 will be administered as an oral daily dose. Patients will undergo titration of SPR001 through three escalating dosage strengths at 2-week intervals. Patients will have overnight PK/PD assessments performed at baseline, which include an pre-dose overnight assessment and a post-dose overnight assessment for PK/PD following administration of the first dose. At the end of each 2-week dosing period, patients will return for single overnight visits for steady-state PK/PD assessments.

A follow-up outpatient visit will occur 30 days after their last dose.

02

Conditions studied

  • Congenital Adrenal Hyperplasia
  • CAH - Congenital Adrenal Hyperplasia

Keywords

  • 17-hydroxyprogesterone
03

Who can participate

Ages eligible
18 Years and older
Sexes eligible
All
Accepts healthy volunteers
No

Inclusion criteria

  • Male and female patients age 18 or older.
  • Documented diagnosis of classic CAH due to 21-hydroxylase deficiency
  • Elevated 17-OHP at screening
  • On a stable glucocorticoid replacement regimen for a minimum of 30 days

Exclusion criteria

Exclusion Criteria:

  • Clinically significant unstable medical condition, illness, or chronic disease
  • Clinically significant psychiatric disorder.
  • Clinically significant abnormal laboratory finding or assessment
  • History of bilateral adrenalectomy or hypopituitarism
  • Pregnant or nursing females
  • Use of any other investigational drug within 30 days
  • Unable to understand and comply with the study procedures, understand the risks, and/or unwilling to provide written informed consent.
04

Study design

Phase
Phase 2
Primary purpose
Treatment
Allocation
Non-randomized
Intervention model
Sequential assignment
Masking
None (open label)
Enrollment
24 participants (actual)

Study arms

  • Experimental
    Cohort A

    The first cohort of 9 patients will be administered SPR001 at dose strength of Dose A daily for 2 weeks, and escalating through Dose B per day for 2 weeks and Dose C per day for 2 weeks.

    Drug: SPR001

  • Experimental
    Cohort B

    Cohort B will begin enrollment after Cohort A has been fully enrolled. Starting dose selection and the stepwise dosing paradigm for Cohort B will be determined by an interim review of safety and PK/PD data from from Cohort A.

    Drug: SPR001

  • Experimental
    Cohort C

    Cohort C will begin enrollment after Cohort B has been fully enrolled. Starting dose selection and the stepwise dosing paradigm for Cohort C will be determined by an interim review of safety and PK/PD data from from Cohort A and B.

    Drug: SPR001

Interventions

  • DrugSPR001

    SPR001 Capsules

05

What researchers measure

Primary outcomes

  1. Safety of SPR001 in Patients With CAH

    Incidence of treatment-emergent adverse events, changes from Baseline to End-of-study in clinical laboratory parameters, physical examination findings, vital signs, ECG parameters

    Time frame: 6 weeks

  2. Change in 17-hydroxyprogesterone

    Change in 17-hydroxyprogesterone from Baseline to End-of-study. Results are expressed as mean percent change from baseline. Reductions in 17-OHP are indicators of better disease control.

    Time frame: Cohort A: Baseline/2a (Day -1-0), First dose/2b (Day 0-1), Visit 3 (Day 13-14), Visit 4 (Day 27-28), Visit 5 (Day 41-42). Cohort B and Cohort C: Visit 2 (Day 0-1), Visit 3 (Day 8), Visit 4 (Day 14-15), Visit 5 (Last dose +30d)

Secondary outcomes

  1. Changes in Pharmacodynamic (PD) Markers

    Changes in adrenocorticotropic hormone (ACTH) and androstenedione (A4) from Baseline to End-of-study are measured in patient serum. Results are expressed as a mean percentage change from baseline. A negative change indicates improvement.

    Time frame: Cohort A: Visit 2a (Day -1 to 0), Visit 2b (Days 0-1), Visit 3 (Day 13-14), Visit 4 (Day 27-28), Visit 5 (Day 41 to 42). Cohorts B+C: Visit 2 (Day 0-1), Visit 3 (Day 8), Visit 4 (Day 27-28), Visit 5 (+30 days after last dose)

  2. Pharmacokinetic Parameter - Maximum Plasma Concentration (Cmax)

    To evaluate the pharmacokinetic (PK) parameter of maximum plasma concentration (Cmax) of SPR001 in patients with CAH.

    Time frame: Serial PK sampling was performed at the end of the 2 weeks for all cohorts and dose levels

  3. Pharmacokinetic Parameter - Area Under the Concentration-time Curve (AUC)

    To evaluate the PK parameter of area under the concentration-time curve (AUC) of SPR001 in patients with CAH

    Time frame: For Cohort A, serial blood collections were made for PK measurements on Day 1 for 200 mg SD and at Week 2 for all QD dose levels. In Cohorts B and C, serial blood samples were drawn for PK measurements at the end of the 2-week treatment period.

06

Results

Posted Oct 22, 2025

Participant flow

No participants enrolled in Period 4: Cohort D

Cohort A
Participant flow — Cohort A
MilestonePeriod 1: Cohort APeriod 2: Cohort BPeriod 3: Cohort CPeriod 4: Cohort D
Started10000
Completed9000
Not completed1000
Withdrew: Lost to follow-up1000
Cohort B
Participant flow — Cohort B
MilestonePeriod 1: Cohort APeriod 2: Cohort BPeriod 3: Cohort CPeriod 4: Cohort D
Started0900
Completed0800
Not completed0100
Withdrew: Discontinued due to sponsor decision0100
Cohort C
Participant flow — Cohort C
MilestonePeriod 1: Cohort APeriod 2: Cohort BPeriod 3: Cohort CPeriod 4: Cohort D
Started0070
Completed0060
Not completed0010

Outcome measures

PrimarySafety of SPR001 in Patients With CAH

Incidence of treatment-emergent adverse events, changes from Baseline to End-of-study in clinical laboratory parameters, physical examination findings, vital signs, ECG parameters

Time frame:
6 weeks
Reported as:
Count of participants · Participants
Safety of SPR001 in Patients With CAH
ParticipantsCohort ACohort BCohort C
Safety of SPR001 in Patients With CAH654
PrimaryChange in 17-hydroxyprogesterone

Change in 17-hydroxyprogesterone from Baseline to End-of-study. Results are expressed as mean percent change from baseline. Reductions in 17-OHP are indicators of better disease control.

Time frame:
Cohort A: Baseline/2a (Day -1-0), First dose/2b (Day 0-1), Visit 3 (Day 13-14), Visit 4 (Day 27-28), Visit 5 (Day 41-42). Cohort B and Cohort C: Visit 2 (Day 0-1), Visit 3 (Day 8), Visit 4 (Day 14-15), Visit 5 (Last dose +30d)
Reported as:
Mean · percentage of mean change from baseline
Change in 17-hydroxyprogesterone
percentage of mean change from baselineCohort BCohort CCohort A - Dose ACohort A - Dose BCohort A - Dose C
Change in 17-hydroxyprogesterone-47.79 ± 63.300-33.19 ± 41.60422.16 ± 172.298-23.71 ± 64.146-13.79 ± 74.742
SecondaryChanges in Pharmacodynamic (PD) Markers

Changes in adrenocorticotropic hormone (ACTH) and androstenedione (A4) from Baseline to End-of-study are measured in patient serum. Results are expressed as a mean percentage change from baseline. A negative change indicates improvement.

Time frame:
Cohort A: Visit 2a (Day -1 to 0), Visit 2b (Days 0-1), Visit 3 (Day 13-14), Visit 4 (Day 27-28), Visit 5 (Day 41 to 42). Cohorts B+C: Visit 2 (Day 0-1), Visit 3 (Day 8), Visit 4 (Day 27-28), Visit 5 (+30 days after last dose)
Reported as:
Mean · percentage of mean change from baseline
Changes in Pharmacodynamic (PD) Markers
percentage of mean change from baselinePD Population Cohort BPD Population Cohort CPD Population - Cohort A Dose APD Population Cohort A - Dose BPD Population - Cohort A - Dose C
Adrenocorticotropic hormone (ACTH)-26.05 ± 54.80716.66 ± 120.211-28.53 ± 53.834-67.60 ± 32.100-36.83 ± 48.510
Androstenedione (A4)-1.58 ± 101.458-30.17 ± 35.055-12.12 ± 47.381-33.18 ± 36.465-28.93 ± 45.167
SecondaryPharmacokinetic Parameter - Maximum Plasma Concentration (Cmax)

To evaluate the pharmacokinetic (PK) parameter of maximum plasma concentration (Cmax) of SPR001 in patients with CAH.

Time frame:
Serial PK sampling was performed at the end of the 2 weeks for all cohorts and dose levels
Reported as:
Mean · ng/dL
Pharmacokinetic Parameter - Maximum Plasma Concentration (Cmax)
ng/dLPK Population Cohort BPK Population Cohort CPK Population - Cohort A Dose APK Population Cohort A - Dose BPK Population - Cohort A - Dose CPK Population Cohort A - Dose A (After single dose)
Pharmacokinetic Parameter - Maximum Plasma Concentration (Cmax)411.25 ± 130.107200.96 ± 132.262283.69 ± 150.116719.30 ± 325.056892.56 ± 289.27296.35 ± 86.1
SecondaryPharmacokinetic Parameter - Area Under the Concentration-time Curve (AUC)

To evaluate the PK parameter of area under the concentration-time curve (AUC) of SPR001 in patients with CAH

Time frame:
For Cohort A, serial blood collections were made for PK measurements on Day 1 for 200 mg SD and at Week 2 for all QD dose levels. In Cohorts B and C, serial blood samples were drawn for PK measurements at the end of the 2-week treatment period.
Reported as:
Mean · ng*hr/dL
Pharmacokinetic Parameter - Area Under the Concentration-time Curve (AUC)
ng*hr/dLPK Population Cohort BPK Population Cohort CPK Population - Cohort A Dose APK Population Cohort A - Dose BPK Population - Cohort A - Dose CPK Population Cohort A - Dose A (After single dose)
Pharmacokinetic Parameter - Area Under the Concentration-time Curve (AUC)2975.968 ± 970.61425.582 ± 941.91881474.162 ± 642.64449.263 ± 1826.48016212.983 ± 2051.9077421.539 ± 331.54

Adverse events

Collected over 6-week treatment period followed by a 4-week washout/safety follow-up period. Non-serious events are listed at a 0% frequency threshold.

Adverse event summary by group
GroupDeathsSeriousOther
Cohort A - Dose A0/10 (0%)0/10 (0%)6/10 (60%)
Cohort A - Dose B0/10 (0%)0/10 (0%)3/10 (30%)
Cohort A - Dose C0/9 (0%)0/10 (0%)3/9 (33.3%)
Cohort B0/9 (0%)0/9 (0%)5/9 (55.6%)
Cohort C0/7 (0%)0/7 (0%)4/7 (57.1%)
Most frequent other events
Showing 10 of 31
Most frequent other events
EventCohort A - Dose ACohort A - Dose BCohort A - Dose CCohort BCohort C
HeadacheNervous system disorders0/100/101/92/90/7
Upper respiratory tract infectionInfections and infestations0/102/100/90/90/7
DisorientationPsychiatric disorders0/100/100/90/91/7
DyspepsiaGastrointestinal disorders0/100/100/90/91/7
ChillsGeneral disorders0/100/100/90/91/7
FatigueGeneral disorders0/100/100/90/91/7
ContusionInjury, poisoning and procedural complications0/100/100/91/91/7
Blood thyroid stimulating hormone increasedInvestigations0/100/100/90/91/7
Pain in extremityMusculoskeletal and connective tissue disorders0/100/100/90/91/7
CoughRespiratory, thoracic and mediastinal disorders0/100/100/90/91/7

Baseline characteristics

24 unique subjects participated in the study; however, two subjects were enrolled in more than one cohort, one subject in Cohorts A and C and one subject in Cohorts A and B. For the subjects enrolled in more than 1 cohort, cohort totals/statistics reflect all baseline values.

Age, Categorical
Age, Categorical(Participants)Cohort ACohort BCohort CCohort DTotal
Cohort A — <=18 years00000
Cohort A — Between 18 and 65 years90009
Cohort A — >=65 years10001
Cohort B — <=18 years00000
Cohort B — Between 18 and 65 years07007
Cohort B — >=65 years01001
Cohort C — <=18 years00000
Cohort C — Between 18 and 65 years00505
Cohort C — >=65 years00101
Sex: Female, Male
Sex: Female, Male(Participants)Cohort ACohort BCohort CCohort DTotal
Cohort A — Female50005
Cohort A — Male50005
Cohort B — Female01001
Cohort B — Male07007
Cohort C — Female00303
Cohort C — Male00303
Ethnicity (NIH/OMB)
Ethnicity (NIH/OMB)(Participants)Cohort ACohort BCohort CCohort DTotal
Cohort A — Hispanic or Latino30003
Cohort A — Not Hispanic or Latino70007
Cohort A — Unknown or Not Reported00000
Cohort B — Hispanic or Latino020—2
Cohort B — Not Hispanic or Latino060—6
Cohort B — Unknown or Not Reported000—0
Cohort C — Hispanic or Latino001—1
Cohort C — Not Hispanic or Latino005—5
Cohort C — Unknown or Not Reported000—0
Race (NIH/OMB)
Race (NIH/OMB)(Participants)Cohort ACohort BCohort CCohort DTotal
Cohort A — American Indian or Alaska Native00000
Cohort A — Asian00000
Cohort A — Native Hawaiian or Other Pacific Islander00000
Cohort A — Black or African American00000
Cohort A — White1000010
Cohort A — More than one race00000
Cohort A — Unknown or Not Reported00000
Cohort B — American Indian or Alaska Native00000
Cohort B — Asian00000
Cohort B — Native Hawaiian or Other Pacific Islander00000
Cohort B — Black or African American00000
Cohort B — White08008
Cohort B — More than one race00000
Cohort B — Unknown or Not Reported00000
Cohort C — American Indian or Alaska Native00000
Cohort C — Asian00000
Cohort C — Native Hawaiian or Other Pacific Islander00000
Cohort C — Black or African American00000
Cohort C — White00505
Cohort C — More than one race00101
Cohort C — Unknown or Not Reported00000
Region of Enrollment
Region of Enrollment(participants)Cohort ACohort BCohort CCohort DTotal
United States1086—24
Body Mass Index (kg/m^2)
Body Mass Index (kg/m^2)(kg/m^2)Cohort ACohort BCohort CCohort DTotal
Mean31.7 ± 11.8030.4 ± 6.3132.3 ± 5.67—31.4 ± 8.44
07

Study locations

9 sites
  • Spruce Biosciences Clinical Site
    Orange, California 92123, United States
  • Spruce Biosciences Clinical Site
    San Diego, California 92123, United States
  • Spruce Biosciences Clinical Site
    Melbourne, Florida 32935, United States
  • Spruce Biosciences Clinical Site
    Atlanta, Georgia 30046, United States
  • Spruce Biosciences Clinical Site
    Indianapolis, Indiana 46202, United States
  • Spruce Biosciences Clinical Site
    Ann Arbor, Michigan 48109, United States
  • Spruce Biosciences Clinical Site
    Minneapolis, Minnesota 55414, United States
  • Spruce Biosciences Clinical Site
    Las Vegas, Nevada 89148, United States
  • Spruce Biosciences Clinical Site
    Philadelphia, Pennsylvania 19104, United States
08

References and documents

Publications

  • Sarafoglou K, Barnes CN, Huang M, Imel EA, Madu IJ, Merke DP, Moriarty D, Nakhle S, Newfield RS, Vogiatzi MG, Auchus RJ. Tildacerfont in Adults With Classic Congenital Adrenal Hyperplasia: Results from Two Phase 2 Studies. J Clin Endocrinol Metab. 2021 Oct 21;106(11):e4666-e4679. doi: 10.1210/clinem/dgab438. PubMed 34146101 ↗

Study documents

  • Study protocol · Aug 23, 2018
  • Statistical analysis plan · May 3, 2019

Documents are hosted by the registry — open the source record to download them.

Individual participant data

Plan to share: No

09

Registry details

Key details

Study ID
NCT03257462
Lead sponsor
Spruce Biosciences
Responsible party
Sponsor
First posted
Aug 22, 2017
Start date
Jul 12, 2017
Primary completion
Mar 2, 2019
Completion
Mar 29, 2019
Results posted
Oct 22, 2025
Last update
Oct 22, 2025

Study contacts

Spruce Chief Medical Officer, MD
study director · Spruce Biosciences
Richard Auchus, MD, PhD
principal investigator · University of Michigan

Oversight

Data monitoring committee
No
FDA-regulated drug
Yes
FDA-regulated device
No
View the source record on ClinicalTrials.gov ↗

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